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Chronic lithium administration in a mouse model for Krabbe disease
Krabbe disease (KD; or globoid cell leukodystrophy) is an autosomal recessive lysosomal storage disorder caused by deficiency of the galactosylceramidase (GALC) enzyme. No cure is currently available for KD. Clinical applied treatments are supportive only. Recently, we demonstrated that two differen...
Autores principales: | Del Grosso, Ambra, Parlanti, Gabriele, Angella, Lucia, Giordano, Nadia, Tonazzini, Ilaria, Ottalagana, Elisa, Carpi, Sara, Pellegrino, Roberto Maria, Alabed, Husam B. R., Emiliani, Carla, Caleo, Matteo, Cecchini, Marco |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley & Sons, Inc.
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8743347/ https://www.ncbi.nlm.nih.gov/pubmed/35028271 http://dx.doi.org/10.1002/jmd2.12258 |
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