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Muscle and Bone Impairment in Infantile Nephropathic Cystinosis: New Concepts
Cystinosis Metabolic Bone Disease (CMBD) has emerged during the last decade as a well-recognized, long-term complication in patients suffering from infantile nephropathic cystinosis (INC), resulting in significant morbidity and impaired quality of life in teenagers and adults with INC. Its underlyin...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8749987/ https://www.ncbi.nlm.nih.gov/pubmed/35011732 http://dx.doi.org/10.3390/cells11010170 |