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Dynamics of skeletal muscle-resident stem cells during myogenesis in fibrodysplasia ossificans progressiva

Fibrodysplasia ossificans progressiva (FOP) is a rare genetic disease in which extraskeletal (heterotopic) bone forms within tissues such as skeletal muscles, often in response to injury. Mutations in the BMP type I receptor ACVR1/ALK2 cause FOP by increasing BMP pathway signaling. In contrast to th...

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Detalles Bibliográficos
Autores principales: Stanley, Alexandra, Tichy, Elisia D., Kocan, Jacob, Roberts, Douglas W., Shore, Eileen M., Mourkioti, Foteini
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Nature Publishing Group UK 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8760285/
https://www.ncbi.nlm.nih.gov/pubmed/35031614
http://dx.doi.org/10.1038/s41536-021-00201-8