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Pericardial Constriction and Myocardial Restriction in Pediatric Mulibrey Nanism: A Complex Disease With Diastolic Dysfunction

BACKGROUND: Mulibrey nanism (MUL) is a rare condition with profound growth delay. Congestive heart failure is a major determinant of prognosis. The aim was to delineate pericardial constriction and myocardial functional abnormalities in a pediatric MUL sample. METHODS: A total of 23 MUL patients and...

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Detalles Bibliográficos
Autores principales: Sarkola, Taisto, Lipsanen-Nyman, Marita, Jalanko, Hannu, Jokinen, Eero
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8767125/
https://www.ncbi.nlm.nih.gov/pubmed/35072025
http://dx.doi.org/10.1016/j.cjco.2021.08.012