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Pericardial Constriction and Myocardial Restriction in Pediatric Mulibrey Nanism: A Complex Disease With Diastolic Dysfunction

BACKGROUND: Mulibrey nanism (MUL) is a rare condition with profound growth delay. Congestive heart failure is a major determinant of prognosis. The aim was to delineate pericardial constriction and myocardial functional abnormalities in a pediatric MUL sample. METHODS: A total of 23 MUL patients and...

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Detalles Bibliográficos
Autores principales:	Sarkola, Taisto, Lipsanen-Nyman, Marita, Jalanko, Hannu, Jokinen, Eero
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Elsevier 2021
Materias:	Original Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8767125/ https://www.ncbi.nlm.nih.gov/pubmed/35072025 http://dx.doi.org/10.1016/j.cjco.2021.08.012

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