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The Multiple Functions of Fibrillin-1 Microfibrils in Organismal Physiology

Fibrillin-1 is the major structural component of the 10 nm-diameter microfibrils that confer key physical and mechanical properties to virtually every tissue, alone and together with elastin in the elastic fibers. Mutations in fibrillin-1 cause pleiotropic manifestations in Marfan syndrome (MFS), in...

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Detalles Bibliográficos
Autores principales: Asano, Keiichi, Cantalupo, Anna, Sedes, Lauriane, Ramirez, Francesco
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8836826/
https://www.ncbi.nlm.nih.gov/pubmed/35163812
http://dx.doi.org/10.3390/ijms23031892