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Natural history of respiratory muscle strength in spinal muscular atrophy: a prospective national cohort study

BACKGROUND: Respiratory complications are the most important cause of morbidity and mortality in spinal muscular atrophy (SMA). Respiratory muscle weakness results in impaired cough, recurrent respiratory tract infections and eventually can cause respiratory failure. We assessed longitudinal pattern...

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Detalles Bibliográficos
Autores principales: Veldhoen, Esther S., Wijngaarde, Camiel A., Hulzebos, Erik H. J., Wösten-van Asperen, Roelie M., Wadman, Renske I., van Eijk, Ruben P. A., Asselman, Fay Lynn, Stam, Marloes, Otto, Louise A. M., Cuppen, Inge, Scheijmans, Feline E. V., den Oudenrijn, Laura P. Verweij-van, Bartels, Bart, Gaytant, Michael A., van der Ent, Cornelis K., van der Pol, W. Ludo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8862532/
https://www.ncbi.nlm.nih.gov/pubmed/35189949
http://dx.doi.org/10.1186/s13023-022-02227-7