In Vivo Metabolic Responses to Different Formulations of Amino Acid Mixtures for the Treatment of Phenylketonuria (PKU)

Phenylketonuria (PKU) is a rare autosomal recessive inborn error of metabolism where the mainstay of treatment is a Phe restricted diet consisting of a combination of limited amounts of natural protein with supplementation of Phe-free or low-Phe protein substitutes and special low protein foods. Sub...

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Detalles Bibliográficos
Autores principales: Giarratana, Nadia, Giardino, Luciana, Bighinati, Andrea, Reiner, Giorgio, Rocha, Júlio César
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2022
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8877664/
https://www.ncbi.nlm.nih.gov/pubmed/35216344
http://dx.doi.org/10.3390/ijms23042227

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8877664/
https://www.ncbi.nlm.nih.gov/pubmed/35216344
http://dx.doi.org/10.3390/ijms23042227

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