Morbidities and mortality in patients with hereditary thrombotic thrombocytopenic purpura

Hereditary thrombotic thrombocytopenic purpura (hTTP) is a rare disorder caused by severe ADAMTS13 deficiency. Major morbidities and death at a young age are common. Although replacement of ADAMTS13 can prevent morbidities and death, current regimens of plasma prophylaxis are insufficient. We identi...

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Detalles Bibliográficos
Autores principales: Borogovac, Azra, Reese, Jessica A., Gupta, Samiksha, George, James N.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: American Society of Hematology 2022
Materias:
Thrombosis and Hemostasis
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8945298/
https://www.ncbi.nlm.nih.gov/pubmed/34807988
http://dx.doi.org/10.1182/bloodadvances.2021005760

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8945298/
https://www.ncbi.nlm.nih.gov/pubmed/34807988
http://dx.doi.org/10.1182/bloodadvances.2021005760

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