Cargando…

Lung Transplantation for Pulmonary Fibrosis Associated With Hermansky-Pudlak Syndrome. A Single-center Experience

Hermansky-Pudlak syndrome (HPS) is an autosomal recessive disorder characterized by oculocutaneous albinism, platelet storage defect with resultant bleeding diathesis, and pulmonary fibrosis. The bleeding diathesis associated with HPS had long been considered a contraindication to lung transplantati...

Descripción completa

Detalles Bibliográficos
Autores principales: Benvenuto, Luke, Qayum, Seema, Kim, Hanyoung, Robbins, Hilary, Shah, Lori, Dimango, Angela, Magda, Gabriela, Grewal, Harpreet, Lemaitre, Philippe, Stanifer, Bryan P., Sonett, Joshua, D’Ovidio, Frank, Arcasoy, Selim M.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Lippincott Williams & Wilkins 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8947604/
https://www.ncbi.nlm.nih.gov/pubmed/35350109
http://dx.doi.org/10.1097/TXD.0000000000001303