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The Effect of CFTR Modulators on Airway Infection in Cystic Fibrosis

The advent of Cystic fibrosis transmembrane receptor (CFTR) modulators in 2012 was a critical event in the history of cystic fibrosis (CF) treatment. Unlike traditional therapies that target downstream effects of CFTR dysfunction, CFTR modulators aim to correct the underlying defect at the protein l...

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Detalles Bibliográficos
Autores principales: Harvey, Caitlyn, Weldon, Sinead, Elborn, Stuart, Downey, Damian G., Taggart, Clifford
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8998472/
https://www.ncbi.nlm.nih.gov/pubmed/35408875
http://dx.doi.org/10.3390/ijms23073513