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Comprehensive clinical, radiological, pathological and biochemical analysis required to differentiate VV1 sporadic Creutzfeldt-Jakob disease from suspected variant CJD

BACKGROUND: A diagnosis of variant Creutzfeldt-Jakob disease (vCJD), the zoonotic prion disease related to transmission of bovine spongiform encephalopathy, can carry enormous public health ramifications. Until recently, all vCJD clinical cases were confined to patients displaying methionine homozyg...

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Detalles Bibliográficos
Autores principales: Holper, Sarah, Lewis, Victoria, Wesselingh, Robb, Gaillard, Frank, Collins, Steven J, Butzkueven, Helmut
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BMJ Publishing Group 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9020293/
https://www.ncbi.nlm.nih.gov/pubmed/35519901
http://dx.doi.org/10.1136/bmjno-2022-000299