Outcomes of Systemic Treatment in Children and Adults With Netherton Syndrome: A Systematic Review

BACKGROUND: Comèl-Netherton syndrome (NS) is a rare disease caused by pathogenic variants in the SPINK5 gene, leading to severe skin barrier impairment and proinflammatory upregulation. Given the severity of the disease, treatment of NS is challenging. Current treatment regimens are mainly topical a...

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Detalles Bibliográficos
Autores principales: Nouwen, Anouk E. M., Schappin, Renske, Nguyen, N. Tan, Ragamin, Aviël, Bygum, Anette, Bodemer, Christine, Dalm, Virgil A. S. H., Pasmans, Suzanne G. M. A.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2022
Materias:
Immunology
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9022473/
https://www.ncbi.nlm.nih.gov/pubmed/35464459
http://dx.doi.org/10.3389/fimmu.2022.864449

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9022473/
https://www.ncbi.nlm.nih.gov/pubmed/35464459
http://dx.doi.org/10.3389/fimmu.2022.864449

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