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Effectiveness of Open Fenestration for Autosomal Dominant Polycystic Liver Disease

Autosomal dominant polycystic liver disease (ADPLD) is a rare disease with variable clinical presentations, characterized by cystic enlargement of the liver. The diagnosis is made based on family history, patient's age, and liver phenotype and is confirmed by imaging tests. The treatment aims t...

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Detalles Bibliográficos
Autores principales: Norcia, Luiz Fernando, Watanabe, Erika Mayumi, Hasimoto, Claudia Nishida, Pelafsky, Leonardo, de Oliveira, Walmar Kerche, Sassaki, Ligia Yukie
Formato: Online Artículo Texto
Lenguaje:English
Publicado: S. Karger AG 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9035950/
https://www.ncbi.nlm.nih.gov/pubmed/35528778
http://dx.doi.org/10.1159/000523662