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A rapid LC-MS/MS assay for detection and monitoring of underivatized branched-chain amino acids in maple syrup urine disease

INTRODUCTION: Quantitation of the isomeric branched-chain amino acids (BCAA; valine, alloisoleucine, isoleucine, leucine) is a challenging task that typically requires derivatization steps or long runtimes if a traditional chromatographic method involving a ninhydrin ion pairing reagent is used. OBJ...

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Detalles Bibliográficos
Autores principales:	Piri-Moghadam, Hamed, Miller, Alan, Pronger, Debra, Vicente, Faye, Charrow, Joel, Haymond, Shannon, Lin, David C.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Elsevier 2022
Materias:	Regular Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9120951/ https://www.ncbi.nlm.nih.gov/pubmed/35602306 http://dx.doi.org/10.1016/j.jmsacl.2022.04.003

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