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Neuroinflammation in Friedreich’s Ataxia

Friedreich’s ataxia (FRDA) is a rare genetic disorder caused by mutations in the gene frataxin, encoding for a mitochondrial protein involved in iron handling and in the biogenesis of iron−sulphur clusters, and leading to progressive nervous system damage. Although the overt manifestations of FRDA i...

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Detalles Bibliográficos
Autores principales: Apolloni, Savina, Milani, Martina, D’Ambrosi, Nadia
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9181348/
https://www.ncbi.nlm.nih.gov/pubmed/35682973
http://dx.doi.org/10.3390/ijms23116297