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An anti-ACVR1 antibody exacerbates heterotopic ossification by fibro-adipogenic progenitors in fibrodysplasia ossificans progressiva mice
Fibrodysplasia ossificans progressiva (FOP) is a rare genetic disease characterized by progressive and catastrophic heterotopic ossification (HO) of skeletal muscle and associated soft tissues. FOP is caused by dominantly acting mutations in the gene encoding the bone morphogenetic protein (BMP) typ...
Autores principales: | Lees-Shepard, John B., Stoessel, Sean J., Chandler, Julian T., Bouchard, Keith, Bento, Patricia, Apuzzo, Lorraine N., Devarakonda, Parvathi M., Hunter, Jeffrey W., Goldhamer, David J. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
American Society for Clinical Investigation
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9197527/ https://www.ncbi.nlm.nih.gov/pubmed/35503416 http://dx.doi.org/10.1172/JCI153795 |
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