Comparison between idiopathic and VEXAS-relapsing polychondritis: analysis of a French case series of 95 patients

OBJECTIVE: A new adult-onset autoinflammatory syndrome has been described, named VEXAS (Vacuoles, E1 Enzyme, X-linked, Autoinflammatory, Somatic). We aimed to compare the clinical characteristics, the laboratory features and the outcomes between idiopathic-relapsing polychondritis (I-RP) and VEXAS-r...

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Detalles Bibliográficos
Autores principales: Khitri, Mohamed-Yacine, Guedon, Alexis F, Georgin-Lavialle, Sophie, Terrier, Benjamin, Saadoun, David, Seguier, Julie, le Besnerais, Maelle, De Moreuil, Claire, Denis, Guillaume, Gerfaud-Valentin, Mathieu, Allain, Jean Sebastien, Maria, Alexandre, Bouillet, Laurence, Grobost, Vincent, Galland, Joris, Kosmider, Olivier, Dumont, Anael, Devaux, Mathilde, Subran, Benjamin, Schmidt, Jean, Marianetti-Guingel, Paola, Audia, Sylvain, Palat, Sylvain, Roux-Sauvat, Marielle, Jachiet, Vincent, Hirsch, Pierre, Fain, Olivier, Mekinian, Arsène
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BMJ Publishing Group 2022
Materias:
Autoinflammatory Disorders
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9315905/
https://www.ncbi.nlm.nih.gov/pubmed/35868738
http://dx.doi.org/10.1136/rmdopen-2022-002255

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9315905/
https://www.ncbi.nlm.nih.gov/pubmed/35868738
http://dx.doi.org/10.1136/rmdopen-2022-002255

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