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Anaesthetic Management in Mucopolysaccharidoses Patients: Clinical Experience in a Tertiary Hospital

Introduction: Mucopolysaccharidoses (MPS) are a group of rare inherited metabolic diseases caused by the deficiency of enzymes required to degrade glycosaminoglycans (GAGs) in the lysosome with progressive and multiorgan involvement. Due to its progressive nature, a large number of patients need sur...

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Detalles Bibliográficos
Autores principales: Machado, Andreia, Rodrigues, Diana, Ferreira, Amélia, Dias, José, Santos, Patrícia
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9421557/
https://www.ncbi.nlm.nih.gov/pubmed/36060393
http://dx.doi.org/10.7759/cureus.27474