Treatment of VLCAD-Deficient Patient Fibroblasts with Peroxisome Proliferator-Activated Receptor δ Agonist Improves Cellular Bioenergetics

Background: Very long-chain acyl-CoA dehydrogenase (VLCAD) deficiency is an autosomal recessive disease that prevents the body from utilizing long-chain fatty acids for energy, most needed during stress and fasting. Symptoms can appear from infancy through childhood and adolescence or early adulthoo...

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Detalles Bibliográficos
Autores principales: D’Annibale, Olivia M., Phua, Yu Leng, Van’t Land, Clinton, Karunanidhi, Anuradha, Dorenbaum, Alejandro, Mohsen, Al-Walid, Vockley, Jerry
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2022
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9454759/
https://www.ncbi.nlm.nih.gov/pubmed/36078043
http://dx.doi.org/10.3390/cells11172635

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9454759/
https://www.ncbi.nlm.nih.gov/pubmed/36078043
http://dx.doi.org/10.3390/cells11172635

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