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OA05 Clinical presentation, risk factors and prognosis of MDA5-positive JDM; clinical diversity and red flags

INTRODUCTION/BACKGROUND: MDA5-positive juvenile dermatomyositis (JDM) represents a distinct clinical phenotype associated with skin and oral ulceration, milder muscle involvement and a higher incidence of interstitial lung disease (ILD) and severe rapidly progressive ILD (RP-ILD). DESCRIPTION/METHOD...

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Detalles Bibliográficos
Autores principales: McLellan, Kirsty, Al-Obaidi, Muthana, Compeyrot-Lacassagne, Sandrine, Pilkington, Clarissa, Moraitis, Elena, Papadopoulou, Charalampia
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9515758/
http://dx.doi.org/10.1093/rap/rkac066.005