Elevated Levels of Toxic Bile Acids in Serum of Cystic Fibrosis Patients with CFTR Mutations Causing Pancreatic Insufficiency

Hepatobiliary involvement is a hallmark in cystic fibrosis (CF), as the causative CF Transmembrane Conductance Regulator (CFTR) defect is expressed in the biliary tree. However, bile acid (BA) compositions in regard to pancreatic insufficiency, which is present at an early stage in about 85% of CF p...

Descripción completa

Detalles Bibliográficos
Autores principales: Tabori, Harold, Schneider, Jochen, Lüth, Stefan, Zagoya, Carlos, Barucha, Anton, Lehmann, Thomas, Kauf, Eberhard, Barth, Astrid, Mainz, Jochen G.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2022
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9603931/
https://www.ncbi.nlm.nih.gov/pubmed/36293293
http://dx.doi.org/10.3390/ijms232012436

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9603931/
https://www.ncbi.nlm.nih.gov/pubmed/36293293
http://dx.doi.org/10.3390/ijms232012436

Ejemplares similares