Beneficial effects of SS-31 peptide on cardiac mitochondrial dysfunction in tafazzin knockdown mice

Barth Syndrome (BTHS), a genetic disease associated with early-onset cardioskeletal myopathy, is caused by loss-of-function mutations of the TAFAZZIN gene, which is responsible for remodeling the mitochondrial phospholipid cardiolipin (CL). Deregulation of CL biosynthesis and maturation in BTHS mito...

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Detalles Bibliográficos
Autores principales: Russo, Silvia, De Rasmo, Domenico, Signorile, Anna, Corcelli, Angela, Lobasso, Simona
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Nature Publishing Group UK 2022
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9674582/
https://www.ncbi.nlm.nih.gov/pubmed/36400945
http://dx.doi.org/10.1038/s41598-022-24231-4

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9674582/
https://www.ncbi.nlm.nih.gov/pubmed/36400945
http://dx.doi.org/10.1038/s41598-022-24231-4

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