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MRI changes in diaphragmatic motion and curvature in Pompe disease over time

OBJECTIVES: To evaluate changes in diaphragmatic function in Pompe disease using MRI over time, both during natural disease course and during treatment with enzyme replacement therapy (ERT). METHODS: In this prospective study, 30 adult Pompe patients and 10 healthy controls underwent pulmonary funct...

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Detalles Bibliográficos
Autores principales: Harlaar, Laurike, Ciet, Pierluigi, van Tulder, Gijs, van Kooten, Harmke A., van der Beek, Nadine A. M. E., Brusse, Esther, de Bruijne, Marleen, Tiddens, Harm A. W. M., van der Ploeg, Ans T., van Doorn, Pieter A.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Springer Berlin Heidelberg 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9705445/
https://www.ncbi.nlm.nih.gov/pubmed/35829785
http://dx.doi.org/10.1007/s00330-022-08940-y