Cargando…

Mucopolysaccharidoses: Cellular Consequences of Glycosaminoglycans Accumulation and Potential Targets

Mucopolysaccharidoses (MPSs) constitute a heterogeneous group of lysosomal storage disorders characterized by the lysosomal accumulation of glycosaminoglycans (GAGs). Although lysosomal dysfunction is mainly affected, several cellular organelles such as mitochondria, endoplasmic reticulum, Golgi app...

Descripción completa

Detalles Bibliográficos
Autores principales: Leal, Andrés Felipe, Benincore-Flórez, Eliana, Rintz, Estera, Herreño-Pachón, Angélica María, Celik, Betul, Ago, Yasuhiko, Alméciga-Díaz, Carlos Javier, Tomatsu, Shunji
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9820209/
https://www.ncbi.nlm.nih.gov/pubmed/36613919
http://dx.doi.org/10.3390/ijms24010477