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Mucopolysaccharidoses: Cellular Consequences of Glycosaminoglycans Accumulation and Potential Targets

Mucopolysaccharidoses (MPSs) constitute a heterogeneous group of lysosomal storage disorders characterized by the lysosomal accumulation of glycosaminoglycans (GAGs). Although lysosomal dysfunction is mainly affected, several cellular organelles such as mitochondria, endoplasmic reticulum, Golgi app...

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Detalles Bibliográficos
Autores principales:	Leal, Andrés Felipe, Benincore-Flórez, Eliana, Rintz, Estera, Herreño-Pachón, Angélica María, Celik, Betul, Ago, Yasuhiko, Alméciga-Díaz, Carlos Javier, Tomatsu, Shunji
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2022
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9820209/ https://www.ncbi.nlm.nih.gov/pubmed/36613919 http://dx.doi.org/10.3390/ijms24010477

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