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Dysregulated Cell Homeostasis and miRNAs in Human iPSC-Derived Cardiomyocytes from a Propionic Acidemia Patient with Cardiomyopathy

Propionic acidemia (PA) disorder shows major involvement of the heart, among other alterations. A significant number of PA patients develop cardiac complications, and available evidence suggests that this cardiac dysfunction is driven mainly by the accumulation of toxic metabolites. To contribute to...

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Detalles Bibliográficos
Autores principales: Álvarez, Mar, Ruiz-Sala, Pedro, Pérez, Belén, Desviat, Lourdes Ruiz, Richard, Eva
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9916417/
https://www.ncbi.nlm.nih.gov/pubmed/36768524
http://dx.doi.org/10.3390/ijms24032182