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Dysregulated Cell Homeostasis and miRNAs in Human iPSC-Derived Cardiomyocytes from a Propionic Acidemia Patient with Cardiomyopathy

Propionic acidemia (PA) disorder shows major involvement of the heart, among other alterations. A significant number of PA patients develop cardiac complications, and available evidence suggests that this cardiac dysfunction is driven mainly by the accumulation of toxic metabolites. To contribute to...

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Detalles Bibliográficos
Autores principales:	Álvarez, Mar, Ruiz-Sala, Pedro, Pérez, Belén, Desviat, Lourdes Ruiz, Richard, Eva
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2023
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9916417/ https://www.ncbi.nlm.nih.gov/pubmed/36768524 http://dx.doi.org/10.3390/ijms24032182

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