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Modeling of Fabry disease nephropathy using patient derived human induced pluripotent stem cells and kidney organoid system

OBJECTIVES: To explore the possibility of kidney organoids generated using patient derived human induced pluripotent stem cells (hiPSC) for modeling of Fabry disease nephropathy (FDN). METHODS: First, we generated hiPSC line using peripheral blood mononuclear cells (PBMCs) from two male FD-patients...

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Detalles Bibliográficos
Autores principales:	Cui, Sheng, Fang, Xianying, Lee, Hanbi, Shin, Yoo Jin, Koh, Eun-Sil, Chung, Sungjin, Park, Hoon Suk, Lim, Sun Woo, Lee, Kang In, Lee, Jae Young, Yang, Chul Woo, Chung, Byung Ha
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2023
Materias:	Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9948377/ https://www.ncbi.nlm.nih.gov/pubmed/36814269 http://dx.doi.org/10.1186/s12967-023-03992-0

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