Cargando…

Case report: HLA-haploidentical HSCT rescued with donor lymphocytes infusions in a patient with X-linked chronic granulomatous disease

Chronic granulomatous disease is an inborn error of immunity due to disrupted function of the nicotinamide adenine dinucleotide phosphate (NADPH) oxidase complex. This results in impaired respiratory burst of phagocytes and insufficient killing of bacteria and fungi. Patients with chronic granulomat...

Descripción completa

Detalles Bibliográficos
Autores principales: Scheiermann, Julia, Künkele, Annette, von Stackelberg, Arend, Eggert, Angelika, Lang, Peter, Zirngibl, Felix, Martin, Luise, Schulte, Johannes Hubertus, von Bernuth, Horst
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9978143/
https://www.ncbi.nlm.nih.gov/pubmed/36875143
http://dx.doi.org/10.3389/fimmu.2023.1042650