Diffuse panniculitis in a teenage male with ZZ α(1)-antitrypsin deficiency

Diffuse panniculitis is a rare manifestation of α(1)-ATD, albeit perhaps the most fulminant and life-threatening complication, associated usually with ZZ phenotype. Intravenous α(1)-AT treatment is lifesaving. https://bit.ly/3EDmCzT

Detalles Bibliográficos
Autores principales: Papiris, Spyros A., Parmaxidis, Anthimos, Theotokoglou, Sofia, Tsakiraki, Zoe, Veith, Martina, Panagiotou, Aikaterini, Pappa, Vasiliki, Kallieri, Maria, Mornex, Jean-François, Katoulis, Alexander C., Haritos, Dionysios, Panayiotides, Ioannis G., Manali, Effrosyni D.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: European Respiratory Society 2023
Materias:
Research Letters
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9986751/
https://www.ncbi.nlm.nih.gov/pubmed/36891069
http://dx.doi.org/10.1183/23120541.00546-2022

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9986751/
https://www.ncbi.nlm.nih.gov/pubmed/36891069
http://dx.doi.org/10.1183/23120541.00546-2022

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