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Diffuse panniculitis in a teenage male with ZZ α(1)-antitrypsin deficiency
Diffuse panniculitis is a rare manifestation of α(1)-ATD, albeit perhaps the most fulminant and life-threatening complication, associated usually with ZZ phenotype. Intravenous α(1)-AT treatment is lifesaving. https://bit.ly/3EDmCzT
| Autores principales: | , , , , , , , , , , , , |
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| Formato: | Online Artículo Texto |
| Lenguaje: | English |
| Publicado: |
European Respiratory Society
2023
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| Materias: | |
| Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9986751/ https://www.ncbi.nlm.nih.gov/pubmed/36891069 http://dx.doi.org/10.1183/23120541.00546-2022 |
| _version_ | 1784901239234887680 |
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| author | Papiris, Spyros A. Parmaxidis, Anthimos Theotokoglou, Sofia Tsakiraki, Zoe Veith, Martina Panagiotou, Aikaterini Pappa, Vasiliki Kallieri, Maria Mornex, Jean-François Katoulis, Alexander C. Haritos, Dionysios Panayiotides, Ioannis G. Manali, Effrosyni D. |
| author_facet | Papiris, Spyros A. Parmaxidis, Anthimos Theotokoglou, Sofia Tsakiraki, Zoe Veith, Martina Panagiotou, Aikaterini Pappa, Vasiliki Kallieri, Maria Mornex, Jean-François Katoulis, Alexander C. Haritos, Dionysios Panayiotides, Ioannis G. Manali, Effrosyni D. |
| author_sort | Papiris, Spyros A. |
| collection | PubMed |
| description | Diffuse panniculitis is a rare manifestation of α(1)-ATD, albeit perhaps the most fulminant and life-threatening complication, associated usually with ZZ phenotype. Intravenous α(1)-AT treatment is lifesaving. https://bit.ly/3EDmCzT |
| format | Online Article Text |
| id | pubmed-9986751 |
| institution | National Center for Biotechnology Information |
| language | English |
| publishDate | 2023 |
| publisher | European Respiratory Society |
| record_format | MEDLINE/PubMed |
| spelling | pubmed-99867512023-03-07 Diffuse panniculitis in a teenage male with ZZ α(1)-antitrypsin deficiency Papiris, Spyros A. Parmaxidis, Anthimos Theotokoglou, Sofia Tsakiraki, Zoe Veith, Martina Panagiotou, Aikaterini Pappa, Vasiliki Kallieri, Maria Mornex, Jean-François Katoulis, Alexander C. Haritos, Dionysios Panayiotides, Ioannis G. Manali, Effrosyni D. ERJ Open Res Research Letters Diffuse panniculitis is a rare manifestation of α(1)-ATD, albeit perhaps the most fulminant and life-threatening complication, associated usually with ZZ phenotype. Intravenous α(1)-AT treatment is lifesaving. https://bit.ly/3EDmCzT European Respiratory Society 2023-03-06 /pmc/articles/PMC9986751/ /pubmed/36891069 http://dx.doi.org/10.1183/23120541.00546-2022 Text en Copyright ©The authors 2023 https://creativecommons.org/licenses/by-nc/4.0/This version is distributed under the terms of the Creative Commons Attribution Non-Commercial Licence 4.0. For commercial reproduction rights and permissions contact permissions@ersnet.org (mailto:permissions@ersnet.org) |
| spellingShingle | Research Letters Papiris, Spyros A. Parmaxidis, Anthimos Theotokoglou, Sofia Tsakiraki, Zoe Veith, Martina Panagiotou, Aikaterini Pappa, Vasiliki Kallieri, Maria Mornex, Jean-François Katoulis, Alexander C. Haritos, Dionysios Panayiotides, Ioannis G. Manali, Effrosyni D. Diffuse panniculitis in a teenage male with ZZ α(1)-antitrypsin deficiency |
| title | Diffuse panniculitis in a teenage male with ZZ α(1)-antitrypsin deficiency |
| title_full | Diffuse panniculitis in a teenage male with ZZ α(1)-antitrypsin deficiency |
| title_fullStr | Diffuse panniculitis in a teenage male with ZZ α(1)-antitrypsin deficiency |
| title_full_unstemmed | Diffuse panniculitis in a teenage male with ZZ α(1)-antitrypsin deficiency |
| title_short | Diffuse panniculitis in a teenage male with ZZ α(1)-antitrypsin deficiency |
| title_sort | diffuse panniculitis in a teenage male with zz α(1)-antitrypsin deficiency |
| topic | Research Letters |
| url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9986751/ https://www.ncbi.nlm.nih.gov/pubmed/36891069 http://dx.doi.org/10.1183/23120541.00546-2022 |
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